Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL) Case 1Case 2Case 3Case 4 A 55-year-old patient with no cardiovascular risk factors presented with recurrent headache. MRI showed a confluent leukoencephalopathy, involving the external capsules and anterior temporal lobes, and lacunar infarcts. There were deep and lobar microhaemorrhages. 50-year-old patient with no cardiovascular risk factors had recurrent strokes. MRI showed a severe burden of small vessel disease, multiple lacunar infarcts and mixed distribution microhaemorrhages. 50-year-old patient presented with a homonymous hemianopia and mixed sensory and motor deficits. MRI showed an acute left thalamic infarct and a diffuse leukoencephalopathy that involved the external capsules and anterior temporal lobes.