Col4a1 related brain small vessel disease

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  • 20-year-old patient presented with transient sensory disturbance affecting the right arm.
  • MRI showed small vessel territory ischaemic damage within the deep grey nuclei and cerebral white matter.
  • Cerebral white matter bulk was reduced.
  • Abnormal gyration in the perirolandic region suggestive an intrauterine vascular event.
  • Genetic testing revealed a COL4A1 mutation.